PRIMARY CARE
Recommendation 1
The causative drug needs to be avoided indefinitely.
DReSS Syndrome
Not Verified
Disease overview
A rare disorder that can affect the skin, blood and any internal organs, most commonly the liver, kidney, lungs and heart. The cause of DReSS is multifactorial involving drug-exposure, genetic predisposition, viral reactivation and immune system responses.
Common symptoms
Most common are a flu-like prodrome of malaisesore throatfever and swollen lymph nodes. Followed by maculopapular or morbilliformurticated papular rashes and full body redness with exfoliative erythroderma. [ ]
WHEN TO SUSPECT
Recommendation 1
The RegiSCAR criteria (Kardaun et al. 2007) and The Japanese Consensus Group criteria (Shiohara et al. 2007).
HOW TO TEST
Recommendation 1
The RegiSCAR criteria (Kardaun et al. 2007) and The Japanese Consensus Group criteria (Shiohara et al. 2007).
TREATMENT
Recommendation 1
Systemic steroids alongside identification and immediate withdrawal the culprit drug.
FURTHER SUPPORT
Recommendation 1
Aziz, Mariam MD and Ishmael, Faoud MD . Referral to Medical Genetics Department, if available. Initial virtual care is also available through organizations like TeleRare Health.
CLINICAL TRIALS
Recommendation 1
2 non-recruting
Sources
No data available
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